CaafimaadkaCudurrada iyo Xaaladaha

Mauriac syndrome ee sonkorowga

Mauriac syndrome - cudur yeesho sida dhibaatooyin ay sabab u tahay daaweynta aan habboonayn ee diabetes da 'yar ah. Waayo, markii ugu horeysay ee cudurka waxaa lagu tilmaamay in 1930 by dhakhtar Faransiis asal Pierre Mauriac. Waxa uu tilmaamay nooca sawirka clinical, taas oo carruurta qaba cudurka macaanka iyo therapy insulin ee la soo dhaafay qiyaasta qaldan, jimicsi qaar ka mid ah calaamadaha dibadda. Wuxuu ogaaday in carruurta oo dhan la mid ah muuqaalka, taasoo ku muuqata in koritaanka, cayilka, horumarinta hooseeyo dhac galmada yihiin.

Sababaha cudurka

Sababta ugu weyn ee dhibaatooyinka daran waa sax ahayn therapy diabetes eryadeen. In cudurkan ganaca aan si fiican u hawlgala, oo aan soo saarin tiro ku filan oo insulin. Sababo la xiriira cudurada ku dhacdaa deficiency glucose unugyada ay sabab u tahay xaqiiqda ah in ay xoogga xaddiyo badan ee dhiigga.

horumarinta syndrome Mauriac in bukaanka qaba diabetes mellitus type 1 waxa uu la xidhiidhaa daaweynta ku filneyn. ilmaha buka qaadashada insulin ku filan muddo dheer ah ay maamulaan, ama loo isticmaalo wax soo saarka oo tayo hooseeyo iyo kuwa xun la safeeyey, taasoo keentay in deficiency ah chronic of insulin.

la'aan joogto ah insulin ah ee jirka ku keenaysaa in habka soo socda:

  • cudurada dheefshiidka, gaar ahaan cudurka shiid carbohydrate.
  • Kordhinta size ee beerka iyo xumaanshaha dufanka leh ay ugu wacan tahay kor u kacay burburka glycogen.
  • Isbeddelka ku Halabuurka dhiig - korodhka in sonkorta dhiigga, kolestarool, acids dufan.

Haddii tani ay tahay ma dhammaan geedi socodka bahal ah ee jirka intii lagu Mauriac syndrome, sidoo kale bukaanka carruurta arkaan leexashooyinkaasi soo socda:

  • wax soo saarka ku filnayn hormoonnada muhiim ah - yaqaano Cortisol, hormone koritaanka, glucagons, iyo sidii natiijo ah oo xadgudub ku ah geedi socodka koritaanka.
  • Burburka borotiinada iyo calcium saarka hodan iyo fosfooraska, lafaha, ugu danbeyn keentay in horumarinta osteoporosis iyo qaar ka mid ah atrophy muruqa.
  • nuugista kari vitamins in xiidmaha.

Cudurku wuxuu sida caadiga ah u muuqato da'doodu u 15-18 sano u dhexeeya, laakiin habka aan shaqeynin badan sidii hore ka bilaabmaa. Waqtigan xaadirka ah, oo lagu daweeyo diabetic hore isticmaalaa diyaarinta casri ah oo si fiican u daahiriyey, kaas oo gebi ahaanba meesha horumarinta Mauriac syndrome.

symptomatology cudurka

diabetes Mauriac Syndrome uu leeyahay tiro ka mid ah saamaynta:

  • Ilmuhu wuxuu ka danbayso in horumarka iyo koboca Iscelin. Inta badan waxaa jira cayilka iyo dherer gaaban. Xaaladdan oo kale, ilmaha jirran waxaa laga yaabaa in ku Hadhi ka danbeeya dhiggooda ah ee koritaanka by 10-30 sentimitir.
  • walise horumarinta galmada (sifooyinka galmada dhacsan iyo maqnaanshaha caadada gabdhaha).
  • qaangaadhnimada muddada dheer.
  • Cayilka, gaar ahaan wajiga iyo jidhka sare leh addimada khafiif ah. carruurta jirran aad ula mid yihiin, waxay leeyihiin "bilaha-qaabeeya" at midba midka kale ee wajiga, qoorta gaaban, baruurta ee hubka, garbaha, caloosha. Qaybta hoose ee jidhka waa mid aad u dhuuban.
  • beerka la kordhiyo la socday wareegga arooriyaha wareegnay.
  • Osteoporosis (hoos gaabis horumarinta unugyada lafta).
  • cudurrada indhaha, oo ay ku jiraan cudurada ileyska, oo markii danbe horumarinta caadka.

, The Mauriac syndrome ugu badan ee carruurta photo ilmaha buka muujinaysaa waxa calaamadaha cudurka.

ogaanshaha cudurka

ogaanshaha ah "Mauriac syndrome" ayaa lagu wadaa calaamadaha cad dibadda ee cudurka, sida: la'aan height da'da, jiritaanka cayilka, gaar ahaan wejiga aan qaan gaarin galmada, kororka cad ee beerka.

Si loo xaqiijiyo cudurka fuliyay baaritaan dhiig, taas oo keentay in daliilka soo socda waa:

  • caddadka gulukooska ee aan degganayn, si ay u muujiyaan ka bootin joogto ah oo weyn, ka dibna hoos.
  • subaga dhiiga xad-dhaaf ah (hyperlipidemia).
  • korodhka A weyn ee heerka kolestaroolka dhiiggaaga (hypercholesterolemia).

Xaaladaha qaarkood, sii baran xinjirta beerka ujeedadaas, in lagula soo baxo load baruurta

cudurka

Waayo, jidhku yar oo uu cudurku waa mid aad u adag. Sida foomka daran cudurka macaanka, waa ay adag tahay in ay mag-. Inta badan sababa aysiidh iyo kooma hyperglycemic.

Mauriac syndrome dhacdaa daran sababta oo ah waxaa dheer ee soo noqnoqda ee cudurada faafa ee kala duwan, iyo sidoo kale hababka lagmamaarmaanna u soo kabashada adag oo muddo dheer ah ee jirka ku.

Mauriac syndrome iyo Nobekura: ekaanshada iyo kala

Mauriac syndrome iyo Nobekura inta badan horumarisa ee carruurnimada, labada cudurada waa dhibaato halis ah oo diabetes in dhacdaa ku saabsan asalka ah ee daaweynta aan habboonayn. Labada syndromes leeyihiin calaamado la siman, waxay ka mid dhimaal koritaanka iyo horumarka galmada, daba qaan, beerka dufan. Xaaladdan oo kale, ugu weyn ee kala duwan yihiin Nobekura syndrome waa la'aanta ah ee baruurta jidhka xad-dhaaf ah. Xaaladdan oo kale, daaweynta ee labada syndromes looga golleeyahay in dhaawac lagu daaweyn jiray sonkorowga.

daaweynta syndrome Mauriac

daaweynta Direct ee syndrome sidan oo kale ma jirin. All therapy loogu talagalay wax ka qabashada sababaha asalka u ah cudurada iyo dhibaatooyinka ka dhigay in iyaga by. Si arrintan loo sameeyo, bukaanka waxa lagu qoray therapy insulin oo sax ah in qiyaasta saxda ah iyo tayada daawooyinka casriga ah.

Si looga hortago lipodystrophy qabtay tiro ka mid ah hababka ka hortag ah, waayo, sababtan aawadeed sida massage, daaweynta dabiiciga ah iyo gooldhalinta for irbado insulin magacaabay. cunto gaar ah loo xilsaari karaa in lagu daro daaweynta, waxaa loo diido cunto oo dhan cuntooyinka ay ku jiraan dufanka xayawaanka. Xaaladdan oo kale, cunto diiradda on cuntooyinka borotiinka iyo carbohydrate.

therapy Medical waxaa sidoo kale loogu tala galay in ay mag horumariyo on asalka ah oo ka mid ah dhibaatooyinka cudurka sababaya for naznachetsya this bukaanka:

  • gepatoprotektorov Admission si loo soo celiyo unugyada beerka.
  • vitamins B si loo soo celiyo shiid caadiga ah.
  • daroogada Complex loogu talagalay caadi heerarka subaga iyo kolestaroolka dhiiggaaga ku jirta.
  • daawooyinka steroid in ay kiciyaan koritaanka jidhka.
  • daawooyinka hormoonnada ah si loo soo celiyo hawlaha galmada muhiim ah.

Ka Hortagga iyo saadaal

Si looga hortago dhibaatooyin khatar ah ee macaanka sida Mauriac syndrome, waxaa lagama maarmaan ah si ay u fuliyaan daaweynta saxda ah ee cudurka sababaya oo looga hortago yaraanta insulin.

Marka daaweynta marka la isku daro ayaa hore u horumariyo syndrome daawooyinka casriga ah saadaal wanaagsan oo ku filan, laakiin haddii dhammaan talooyinka dhakhtarka. qiyaasta saxda ah ee insulin iyo soo celinta shaqeynayaan dhammaan xubnaha saameeyeen ay awoodaan in ay soo noqdaan caafimaadka ilmaha, labada dibadda iyo gudaha.

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