Inkaar of Ondine - xibin gal

Wixii qarniyo, dadka, isku dayayaan in ay fahmaan oo ay u bartey sharxi arrin qalaad naftooda, lagu baddalo mas'uuliyadda si ay u ilaahyada, jinni dabeecadda iyo kale xayawaan asalka ah. Xataa dadka maanta mar walba ma isla markiiba ay ogaadaan in Lacanadda Ondine - neefsashada joojinta syndrome iyo geeri lama filaan ah - qaar ka mid ah oo aan habaar qadiimiga ah ama dhibaato casri kasta fahmayn, cudurka sababa muuqaalada qaar ka mid ah dadka qaar. Waa maxay cudurka this, sida ay u muuqato iyo in aad u qaban karaa? Waxaan isku dayi doonaa in aan ka jawaabo su'aalaha oo dhan lagu soo qaaday this article.

Halyeeyga An qadiimiga ah

Dhaqaatiirta iyo cilmi ilaa bilowgii qarnigii XX ah oo aan fahmi waayey waxa ay yihiin sababaha keenaya inkaartii Ondine syndrome - joojiyo neefsiga ee aan dhaqdhaqaaqa hurdada, taasoo keentay in dhimashada dhallaanka iyo carruurta yar yar labadaba, iyo dadka waaweyn ee da'da ah oo dhan.

Magaca this ifafaale siiyey halyeeyga ah jir Jarmal ah oo ku saabsan jacaylka mermaids Undine iyo geesigeeda ee Guldbrandta Ringshtettenskogo. Sida ay legend this, gabadhii ayaa diiday inuu gashado si ay iyada jecel yahay noqon. Ka hor inta geesigeeda meesha allabariga ku dhaartay in ay iyada jecel ilaa neefsan karaan. Si kastaba ha ahaatee, jacaylka ragga waaweyn si deg deg ah halkii ay mareen, oo waxay ku beddeleen Undine ah. gabareeymaanyo Bal maxaan u dhiman - waa aan la aqoon, laakiin jirkeeda laga helay biyaha Danube. Ninkeeda qalbi qaboojiyey Guldbrandt si deg deg ah soo jiidasho leh iyo, halmaamay dhaartii, cusub guursaday. Ondine muuqasho ma cafi khiyaanada, u muuqday in geesigeeda a, wuxuu habaaray isaga, keenaya saacad in la xasuusto in aad neefsato. Taas darteed, geesigeeda seexan kari waayay, maxaa yeelay, gama'did, kolkiiba ayuu u dhiman doono, anoo joojinaya inaan neefsado.

dhakhtarro Maanta magacaabi habaar Ondine a - xibin gal syndrome. In cudurkan ee aadanuhu marka la seexdo dhacaya joojinta miyir iyo caasiyoobay ee neefsashada.

Maxaa ku dhacaya bukaanka?

Qubarada ayaa sheegaya in kasta oo xataa gebi ahaanba dadka caafimaadka qaba habeenkii joojiyo neefsashada 10-20 ilbiriqsi. Ma jiraan wax qalad ah ay tahay, maxaa yeelay, ka dibna ku hawl neefsashada caadiga ah waa lay soo celiyey. u shaqeeyo waa dadka horumariyo inkaartii Ondine syndrome, ma waxaa ka mid ah ma hab "automatic" control neefta.

madax bannaan Neefta qofka oo aan awoodo, oo halkaas waa hypoventilation gobolka disritmicheskoy, ama in ka badan si fudud - Dahay. Xaaladdan oo kale jirka uu helo tiro aad u yar oo ah ogsijiin, taas oo horseedaysa rabshooyin iyo cillad ka mid ah xubnaha gudaha iyo nidaamka.

Waa maxay sababta?

Muddo sanado ah, saynisyahano iyo dhakhtarro dalal badan ayaa isku dayay inay ka jawaabaan su'aasha ah waxa syndrome waa "inkaar of Ondine" iyo in la fahmo sababaha. horumar degdeg ah ugu horeysay ee daraasadda cudurka la sameeyey by saynisyahano Sevringausom iyo Mitchell qeybtii labaad ee qarnigii XX ah oo sabab u ah daraasadda bukaannada qaba dhaawaca maskaxda oo daran ay sabab u tahay taas oo uu ku badiyay ay gacanta si toos ah neefsashadaada u gaar ah. Cilmi baadhayaashu waxay ahaayeen awoodaan in la dhiso in Lacanadda Ondine syndrome - nooc ka mid ah cudurka sida xibin gal, hurdo syndrome. Si kastaba ha ahaatee, inuu ka jawaabo su'aasha ah sababta cudurka this saameeyaa dadka caadiga ah, culumadu aysan awoodin in ay.

Eeda hiddo?

Up to our maalmood, dhakhaatiirta ay awoodi waayeen in ay aqoonsadaan sababaha asalka u ah this syndrome. More dhawaan, ka saynisyahano Faransiis ay awoodaan in ay helaan "mujrim" neefsashada stop. Waxay heleen hiddo Thox2B. Sidaa darteed, habaarkii Ondine syndrome cadeeyay inuu yahay cudur hidde, ma la iska dhaxlo, laakiin waxa uu yeeshay ee embriyaha muddada dhalmada ka hor.

Maxaa badbaadin karin?

Haddii in maalmaha jir, caruurta sida syndrome ciday ku dhiman, laakiin dhakhaatiirta maanta caawin kara bukaanka sida ay u noolaadaan si qaangaarnimada, oo isticmaalaya hababka soo socda:

• galinta tuubo dhuunta (tracheostomy) iyo xira bukaanka u neefsashada ;
• maalin walba ka hor inta sariirta aadin in aad xirato weji hawo on ilmaha ee.

dhakhaatiir Jarmal ayaa soo saartay hab lagu galaha laxanka neefsashada ah digir stimulator galay jidhka, in bukaanka loo oggolaado in ay nolol caadi ku dhow. Nuxurka habka been in xaqiiqda ah in inta lagu guda jiro qalliinka yar ee dareemaha phrenic waxaa nimo koronto oo gaar ah, taas oo dejisa waxqabadka neefsashada marka la seexdo.

daawo Modern ma bixin karo daaweynta kasta oo kale oo inkaartii Ondine syndrome, sababta oo ah waxay si fudud aan wali soo bixin.

kooxaha halista

Wajahay cudurka this karaa qof kasta oo inaga mid ah. Dhab ahaantii, dadka waaweyn waxaa dhif ah saameeyeen cudurka this sabab u fudud, laakiin aad looga cabsado ee la soo dhaafay, bukaanka si fudud ma noolaan qaangaarnimada, dhimanayaan hurdadii. Inta badan inkaartii Ondine syndrome waxaa lagu gartaa in dhalaanka iyo carruurta yaryar. Laakiin dadka da'da dhexe iyo wixii ka weyn, iyo sannadihii la soo dhaafay, iyo wiilasha xanuunsado tan iyo noocyada kale ee inkaar Ondine - hurdo xibin gal syndrome (SAS).

xibin gal syndrome

Ka sokow syndrome Ondine kor lagu sharaxay, waxaa jira dhawr nooc oo xibin gal, hurdo (neefsashada xanuunada inta lagu guda jiro waxqabad hurdo):

1. Central.
2. Obstructive ama durugsan.
3. Isku qasan.

Inta badan oo naga mid ah ma aha xataa ogayn, si joogta ah isku dhaceen cudurka nolol maalmeedka. Waxaa la khuurada, taas oo ah mid ka mid ah calaamadaha iyo daliilka xibin gal durugsan.

Ha ka fikiro si aynu si faahfaahsan faraqa u dhexeeya cudurada dhaqdhaqaaqa neefsiga hurdada kor ku xusan.

xibin gal durugsan

Noocan ah neefsashada hawlaha disorder - xaalad nafta halis, oo waxaa lagu gartaa aad u soo noqnoqda, in ka badan 15 jeer saacaddiiba, iyo kala go 'halkii dheer in dhaqdhaqaaqa neefsiga ah in ka badan 10 ilbiriqsi. xibin gal noocan oo kale ah kiisaska intooda badan waa ay sabab u tahay xadgudub ka dhan ah maris ah falalkooda dareemaha bartamaha ee maskaxda in muruqyada ku lug neefsashada. Dhab ahaantii, khuurada waxaa keeni kara iyo muuqaalada jidh ee qaab-dhismeedka bacaraarka, laakiin inta badan noocan ah ee cudurka - inkaartii Ondine - neuropathology, rabshooyin dhaxgalka ee nidaamka dhexe ee habdhiska (nerve system).

view Dhexe

Si ka duwan durugsan ah, noocan ah ee xibin gal dhacaa sabab u tahay noocyo kala duwan oo isbedel bahal ah ee maskaxda ku jira ay sabab u tahay cudur ah, qalliin ama dhaawacyada. Xaaladdan oo kale, ma jiro dadaal neefsashada, sida hawo aan kaakicin falalkooda ka habka dhexe ee neerfayaasha.

xibin gal Mixed ayaa magaceedii ka xaqiiqda ah helay in this syndrome hurdo calaamadaha xibin gal show of nooca dhexe iyo durugsan labadaba. Inta badan, noocan ah xad gudub ku ah dhaqdhaqaaqa neefsiga waxaa laga helaa oo laga helay in sannadka ugu horeeya ee nolosha carruurta.

calaamado khatar ah

Waxaa jira tiro ka mid ah calaamadaha, mid ka mid ah ayaa sheegay in adiga ama dadka aad jeceshahay ee, waa in aad had iyo jeer la tasho dhakhtar,

1. daal joogto ah iyo daal.
2. Dhantaalan dareenka iyo xusuusta.
3. hurdo Chronic, ma dhacday ka dib markii hurdo dheer.
4. hurdo baaxaa iyo jeedisay noqnoqda.
5. Khuurada.
6. madax xanuun subax Baxayn.

Khatarta ay leedahay nooc kasta oo xibin gal ay tahay in habeenkii jidhku ma helo nasasho ku habboon sida unugyada, xubnaha iyo nidaamyada shaqeeyaan hab "degdegga ah" sabab u ah heerka ogsijiin yar yahay, iyaguna way yimaadeen.

Horumarinta muddo dheer, xibin gal, hurdo syndrome si weyn u kordhiyaa halista cudurada wadnaha, hormoonada jidhka, neerfayaasha iyo hababka kale ee jirka.

Dabcan, inta badan calaamadaha sidoo kale ku dhici kara cudurro kale, laakiin waxaa wanaagsan in la caddeeyo cudurka by takhasus u leh.