Hemosiderosis sambabada: Calaamadaha iyo daaweynta

Hemosiderosis sambabada - cudur aad u daran. Waxay dhacdaa marka mass ka mid ah unugyada dhiigga cas xiriir la unugyada ee sambabada aadanaha. Marka tani sii socoto muddo dheer horumarinta Midabka hemosiderin ka kooban birta.

Waa maxay hemosiderosis?

Si loo ogaado cudurkan ayaa suuragal ah keliya ku saleysan X-ray, si kastaba ha ahaatee, waxaa jira calaamado badan kaas oo ay joogaan la malaysan karin. calaamadaha kala in sambabada bukaanka gemosiderkoz - qufac xun, ilaa macne dhiigga, neefta oo ku qabata, dhiig sambabada. Waxaa laga yaabaa in qandho iyo tachycardia.

On ku salaysan X-ray dhakhtarka sambabada ka dhigi kara cudurka la hubo. waxbarashada kale ayaa sidoo kale la sameeyay si loo xaqiijiyo in xanuunka haya bukaanka cudurkan waa. Waa baaritaanka xaakada, chemistry dhiig, xaaladaha daran - biopsy sambabada.

Daaweynta cudurka saaray codsiga ah ee corticosteroids iyo daroogada in la baabi'iyo calaamado gaar ah.

muujinta cudurka

hemosiderosis pulmonary Idiopathic waxaa kaloo loo yaqaan syndrome ujeedo-Gellerstedta. Tani waa dhibaato bahal ah, taas oo u muuqato sabab u ah dhigaalka ah hemosiderin Midabka gaarka ah ee sambabada ah aadanaha. feature ugu weyn ee Midabka this ee xaqiiqda ah in uu ka kooban yahay xabagta bir ah. Wuxuu mas'uul ka yahay kaydinta bir ah ee jirka ku jira. Inta lagu jiro cudurro kala duwan u ururayaa in nudaha ku, taas oo horseedaysa in ay dhibaatooyin caafimaad oo bukaan-socodka. Sidoo kale, waxa ay gaari karaan in meydadka aadanaha.

At ay asaasiga ah, hemosiderin - foomamka lagu kaydiyaa jirka birta firaaqada. Sababta oo ah dhar this leeyihiin cado ah kaga hadlay daxalaystay. Marka qof uu yeesho hemosiderosis pulmonary idiopathic, in unugyada jirka ka gaari karaan ilaa iyo shan garaam oo bir ah.

laftiisa By raasamaal birta khasab ma aha saamayn ku shaqaynaya oo ka mid ah waxyaabaha asaasiga ah ee jirka ku, haddii ay taasi ku sambabada. Si kastaba ha ahaatee, haddii ay weheliyaan sclerosis hemosiderosis pulmonary, cudurada functional ah ee jirka ku lama huraan.

Halis bukaanka u nugul cudurka this yihiin carruurta yaryar iyo dhallinyarada. More inta badan dheddigga.

Sababaha cudurka

Hemosiderosis sambabada dhici kartaa in aadanuhu sababo kala duwan. Kuwa ugu badan - cillad lagu dhasho ee darbiyada markabka ee wareegga pulmonary ah. Taas darteed, jidhka ku jiro daaqa ah qubaan iyo joojinta ku meel gaadhka ah ee socodka dhiigga. Sidaas awgeed exuded erythrocytes, iyo sambabada unugyada waa microbleeds sambabada soo noqnoqda.

Sidaas darteed bir ah tani waxaa la sii daayay oo ku dhacaa hemosiderin ah. Waxa uu, ka bacdi, waxaa nuugo macrophages alveolar iyo shubo ee epithelia iyo unugyada endothelial ka badan ballaaran. Sidoo kale door khaas ah waa cillad kale ee lagu dhasho. xiriir haleysan u dhexeeya labada, kiiskan - halbowleyaasha bronki iyo xididdada sambabka.

dabeecadda Immunoallergic cudurka

Sababaha iyo morphogenesis of hemosiderosis sambabada ayaa sidoo kale laga yaabaa in immunoallergic. Marka ay tani kaxeynayo difaaca keenin dhaawac derbiyada weyn ee qalintaanka pulmonary. Waxaa jira xadgudub ku ah ay hawlgal caadi ah, iyada oo xididdada dhiigga burburay ee sanbabada ayaa waxaa dhaco bir ah xad-dhaaf ah, taasoo keentay in shaqada jirka si dhab ah ugu rabshaysan tahay.

Sidoo kale, dhigaalka-dhaafka ah ee hemosiderin in unugyada sambabada kordhinayaan in geeddi-socodka deg deg ah ee burburinta ah unugyada dhiigga cas, oo ay la socdaan la sii daayo hemoglobin, taas oo dhacda in caajisnimo ah. heerka A sare ee nuugista birta mindhicirka, sii dheerayn isticmaalka daroogada la content a birta sare.

Marka marxaladdan hore ee hemosiderosis pulmonary carruurta dhici karaan sida cudur idiopathic in aan la xiriira dhibaatooyin kale. A waxaa la socon kara by syndrome ee Gainer (lacala haddii jidhku waa mid aad u xasaasi u ah borotiinka ku jira caanaha bovine dabiiciga ah).

Haddii hemosiderosis mar kale ku dhacdaa, mikrokrovotecheniya sambabada waxay keeni kartaa dhiig kar sare, taas oo noqon kara dhibaato chronic.

Sidoo kale, cudurka waxaa la socon kara by syndrome ee Goodpasture. Tani waxay soo gaartay oo ka mid ah Alfiyoli ee sambabada iyo kelyaha, Ulasocto ay nabarro. Cudurku wuxuu inta badan ku xiran yahay ragga ay da'doodu u dhaxayso 20 ilaa 30 sano. Waxaa jira ra'yi ku saabsan nooca la iska dhaxlo.

hemosiderosis fadhiya

hemosiderosis pulmonary Idiopathic in caruurta waxaa inta badan keena cudurada. Waxay noqon kartaa sida ugu fudud SARS, iyo sidoo kale cudurka ka sii daran - jadeecada, xiiq-dheerta iyo duumada. Sidoo kale, waxa laga yaabaa in cawaaqib sarkhaan.

hemosiderosis fadhiya yeesho dhibaatooyinka wadnaha. Waxay noqon kartaa cayn kasta oo cudurka wadnaha - cudurada wadnaha, wadnaha iyo cudurrada kale ee.

sababaha soo noqnoqda soo noqnoqda iyo hemosiderosis fadhiya taag-gaadhista sii dheerayn marka heerkulku hooseeyo, dhaawac jireed ama maskaxeed xoog, isticmaalka daawooyinka qaarkood.

Haddii hemosiderosis socodka gudaha Alfiyoli sambabada, in sawiro si cad u raad muuqda oo microbleeds iyo meel kayd-dhaafka ah ee hemosiderin la mid ah qanjira, oo waxaa lagu abaabulaa xarunta dacallada ka mid ah sambabada yihiin.

calaamadaha

Hemosiderosis ku dhici kara dhowr qaab. Xiisad, subacute oo soo noqnoqonaysa. Haddii cudurka la arko in caruurta, inta badan waxay dhacdaa sida ugu da'da xannaanada, tan iyo intii saddex sannadood ah. Si kastaba ha ahaatee, waxaa jira bukaanada kan cudurka waxaa la dhigay toddobaad ee ugu horreeya ee nolosha.

cudurka muujiyey hemorrhage pulmonary iyo dhiig, dareen ah neefta.

Inta lagu guda jiro dhacdo ee dhibaatooyinka ee aadanuhu u muuqataa qufac culus midabka daxalaystay, in xaaladaha ba'an, waxaa la soo qufacaysid karaa dhiigga. In carruurta yaryar, dhiigga wuxuu noqon karaa in mantaggiisa ku.

On baaritaan, dhakhaatiirta fiiro gaar ah u hinraagid, tachycardia, qandho, inta badan bukaanka ka cabanaya xanuunka xabadka iyo caloosha, iyo sidoo kale ku jira laabatooyinka ee. Waxa kale oo laga yaabaa in la wayneeyo aan caadi ahayn oo ka mid ah beerka iyo dhibicda af badan ee miisaanka.

Haddii hemoptysis sii waqti dheer, bukaanka waxa uu yeeshay dhiig, tabar iyo wareer. maqaarka uu noqdo cirro leh, iyo agagaarka indhaha jiro jaalle sifo. Ninka la daal si dhakhso ah oo joogto ah sanqadh in dhegaha maqlaa. muddo culus oo cudurka ku dhici kara ka dhowr saacadood in ay 10-15 maalmood. Sidaa darteed, waxaa jira ma aan samayn karo aan lahayn daryeel caafimaad.

Inta lagu jiro mudada sii xumaanaysa qufac iyo neefta oo ku qabata hoos u dhici doono, laakiin waa adag tahay ma yididiilo leh, si ay u arkaan dhakhtar waxa loo baahan yahay si degdeg ah. Ee dembidhaafkooda cabashada laga yaabaa in aanay heli karaa oo dhan, iyo qofka u horseedi karaa nolol buuxda shaqaynaya.

Iyada oo sii daridda kasta oo waqti dembidhaafka cudurka waa la dhimay, laakiin saamiga in la kordhiyo muddada iyo adkaanta dhibaatooyinka. Mid ka mid ah cawaaqibka anemia - yaraadan guud ee jidhka. Marar dhif ah, xitaa dhimasho suurto galka ah ee bukaanka - natiijo murugo dhici kartaa sababta oo ah ba'an hemorrhage pulmonary oo lama filaan ah ay neefta.

hemosiderosis cudurka

Si aad u sax ah uu sheego hemosiderosis pulmonary, waxaad u baahan tahay talo-bixin cilmiyaysan oo ah khubaro badan. First of dhan, waa pulmonologist, hematologist. Iyo sidoo kale u baahan inaad wax ka barato daliilka kiliinikada ee cudurka. ma aan samayn karo aan lahayn waxbarasho ee X-rays, falanqaynta xaako, dhiig (sida falanqaynta guud, iyo lagmamaarmaanna) iyo biopsy sambabada.

Si loo ogaado cudurkan waa mid aad u adag. Inta badan qaadan bilood ama xataa sanado ka hor khubaro u tilmaantid cudurka. Mararka qaarkood isaga, darjada saaray. Waxa ay tahay in marka hore ay tahay mid aan astaamo gaar ah, oo la mid ah cudurrada kale oo badan, iyo dad badan oo kaliya ma iyaga siin qiimaha. Sida caadiga ah waxa kaliya xanuun neef-mareenka ku weheliyay qufac iyo dhiig la'aan.

wajiga ba'an

Haddii dhakhaatiirta cudurka hemosiderosis pulmonary idiopathic, daaweynta loo baahan yahay. jirka laftiisa ma qaadi karto dhibaato this. In foomka ba'an cudurka waxaa ku weheliyay crackles iyo wadno garaac. Isla mar ahaantaana la dhimay heerka unugyada dhiigga cas, heerar sare oo bilirubin bir ah serum ee dhiiga waa ay yar tahay.

Marka ay dhibaatooyinka ka dhacaan leukocytosis, heerka ESR soo baxdo, taas oo sida caadiga ah waxay muujinaysaa barar ah. Marxaladaha dambe cudurka u muuqataa polycythemia. Waa geedi socod buro-caanood, Ulasocto kelyaha unugyada dhuuxa lafaha.

waxbarashada X-ray

In daraasadda ee X-rays ee marxaladaha hore ee cudurka lagu gartaa hoos u dhac ee daahfurnaanta of beeraha sambabada. Isla mar ahaantaana, on marxaladaha saddexaad iyo kan afraad waa madoobaato daran fiirsanayo iyo lesions of unugyo la nabarradii sifo.

Inta badan waxaa jira hooskii cusub focal, inkastoo xaqiiqda ah in jirka ay suulaan. On spirography neefsigu muuqata, on wadnaha ah - miokardiostrofiya. cudurka Final ka caawisaa biopsy sambabada.

daaweynta hemosiderosis

daaweynta Successful cudurka tani tahay oo kaliya suurto gal ah marka koorsooyinka daaweyn muddada-dheer ee corticosteroids. Tusaale ahaan, "prednisolone" caawisaa daaweeyo hemosiderosis pulmonary. Daawada yaraynaysaa permeability marinnada dhiigga iyo hakiyo horumarinta reactions, shalalka.

Haddii daaweyn muxaafidka ah ayaa loo aqoonsan yahay in ay ka gadanayaa, hababka qalliinka ka dibna waxaa loo isticmaalaa. Waxaa laga yaabaa in si buuxda ama qayb ahaan laga saaray caajisnimo ah, waxaa si weyn hoos ugu dhigi kartaa halista ah ee remissions. Sidoo kale waxa ay yaraynaysaa suurtagalnimada of dhibaatooyinka, iyo cimri bukaanka qaliinka ka dib markii kordhin doonaa by 7-10 sano.

Diyaargaraw in wajiga ba'an ee horumarinta cudurka

Waxaa xusid mudan in wajiga ba'an iyo ka hortagga daroogada la mid ah soo qoray. Marka cudurka of "hemosiderosis pulmonary" daaweynta dhaqanka wax ku ool ah oo ay isku-dar ah wakiilada cytostatic iyo plasmapheresis. Tani waxa ay yaraynaysaa muuqaalka kore ee autoantibodies cusub oo kaa caawin jidhka qabsadaan jir ah.

Waxaa sidoo kale waa hab wax ku ool ah - saarista bir ah kaadida, waxaa loo isticmaalaa faleebo this "Desferal". In daaweynta calaamadaha isticmaalo bronchodilators, antikoagulyarnye ka dhigan tahay.

dhakhtarro dembidhaafka muddada dheer gaari karo, halka ixtiraamida bukaanada ay cunto adag in reebaysa dhamaan waxyaabaha ku salaysan caanaha lo'da. Haddii cudurka biyaa galay marxaladda chronic, laga yaabee in magacaabidda Nitrate. waxaa gaar ahaan la xidhiidha dhibaatooyinka wadnaha.

noocyada hemosiderosis

Dhakhaatiirta jira noocyo dhowr ah oo cudurkan. Gaar ahaan, hemosiderosis pulmonary lagu gartaa (macropreparations "Brown induration iftiin"). Xaaladdan oo kale, sambabada cabbirkoodu wuu kordhaa, waxay leeyihiin dareen taabasho ah oo aad u cufan. Sidoo kale, mugdiga-cas si brown in ku dhow on lakabka anfac badan qeybaha kala dareemi iyo inclusions brownish.

Waxa kale oo laga yaabaa inuu dhaco sambabada hemosiderosis (micropreparations № 111). Xaaladdan oo kale, pigments brown la arki karo gudaha unugyada iyo dibadda in inta lagu guda jiro Perls reaction shaybaarka noqdo buluug ama cagaar. Waxay kac u dhaxaysa godadka hawomareenno iyo Alfiyoli.

Waxaa intaa dheer, weelashuna waa sambabka aadanaha waa mid aad u weyneyn iyo cidhiidhiga ah. cudurka waxaa la socda dhiig badan Risaalo ka dhexeeya Alfiyoli ah. Isla mar ahaantaana ay ogaadeen lakabka of unugyo.